Cystic Fibrosis

HomePatientsLung Disease Week at the ATS2016Cystic Fibrosis ▶ Information for Experts
Information for Experts

Cystic Fibrosis Week

 

ClinicianATS Educational Products

 

A7 ATS MYTHBUSTER: REVERSING FIBROSIS IN THE LUNGS IS BIOLOGICAL MISSION (IM)POSSIBLE
A92 HOW TO CURE A LUNG DISEASE: THE CYSTIC FIBROSIS STORY
D82 CHALLENGES AND CONSIDERATIONS IN THE MANAGEMENT OF PATIENTS WITH CYSTIC FIBROSIS: BEYOND ROUTINE CARE AND EXACERBATIONS
PG6 MANAGING CYSTIC FIBROSIS IN 2015: WHAT THE PULMONARY PHYSICIAN NEEDS TO KNOW
WS7 MANAGEMENT OF OLDER ADULTS WITH CYSTIC FIBROSIS

 


 

ClinicianATS Journal articles on Cystic Fibrosis

 

American Journal of Respiratory and Critical Care Medicine

Lung Clearance Index and Structural Lung Disease on Computed Tomography in Early Cystic Fibrosis
Vol. 193, No. 1 (2016), pp. 60-67.
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Morphometric Analysis of Explant Lungs in Cystic Fibrosis.
(2015
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X-Box–Binding Protein 1 and Innate Immune Responses of Human Cystic Fibrosis Alveolar Macrophages
Vol. 192, No. 12 (2015), pp. 1449-146.
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The Role of Short-Chain Fatty Acids, Produced by Anaerobic Bacteria, in the Cystic Fibrosis Airway
Vol. 192, No. 11 (2015), pp. 1314-1324.
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Regulatory T-Cell Impairment in Cystic Fibrosis Patients with Chronic Pseudomonas Infection
Vol. 191, No. 8 (2015), pp. 914-923.
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Sustained Benefit from Ivacaftor Demonstrated by Combining Clinical Trial and Cystic Fibrosis Patient Registry Data
(2015)
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Development of the Nasopharyngeal Microbiota in Infants with Cystic Fibrosis
(2015)
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Mutations of Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Gene Cause a Monocyte-selective Adhesion Deficiency
(2015)
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Hypoxic Epithelial Necrosis Triggers Neutrophilic Inflammation via IL-1 Receptor Signaling in Cystic Fibrosis Lung Disease
Vol. 191, No. 8 (2015), pp. 902-913.
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Diabetes-related Mortality in Adults with Cystic Fibrosis. Role of Genotype and Sex
Vol. 191, No. 2 (2015), pp. 194-200.
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American Journal of Respiratory Cell and Molecular Biology

Flow Cytometric Analysis of Myeloid Cells in Human Blood, Bronchoalveolar Lavage, and Lung Tissues
Vol. 54, No. 1 (2016), pp. 13-24.
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Polymorphisms Associated with Expression of BPIFA1/BPIFB1 and Lung Disease Severity in Cystic Fibrosis
Vol. 53, No. 5 (2015), pp. 607-614
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Quantitative Proteomics Reveals an Altered Cystic Fibrosis In Vitro Bronchial Epithelial Secretome
Vol. 53, No. 1 (2015), pp. 22-32.
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Proresolving Action of Docosahexaenoic Acid Monoglyceride in Lung Inflammatory Models Related to Cystic Fibrosis
Vol. 53, No. 4 (2015), pp. 574-583.
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Defective Innate Immunity and Hyperinflammation in Newborn Cystic Fibrosis Transmembrane Conductance Regulator–Knockout Ferret Lungs
Vol. 53, No. 6 (2015), pp. 853-862.
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Role of Exchange Protein Activated by cAMP 1 in Regulating Rates of Microtubule Formation in Cystic Fibrosis Epithelial Cells
Vol. 51, No. 2 (2014), pp. 178-190.
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Anti-inflammatory and Antimicrobial Effects of Thiocyanate in a Cystic Fibrosis Mouse Model
Vol. 53, No. 2 (2015), pp. 193-205.
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Noninvasive Imaging of Experimental Lung Fibrosis
Vol. 53, No. 1 (2015), pp. 8-13.
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Lung Phenotype of Juvenile and Adult Cystic Fibrosis Transmembrane Conductance Regulator–Knockout Ferrets
Vol. 50, No. 3 (2014), pp. 502-512.
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A Genomic Signature Approach to Rescue ΔF508-Cystic Fibrosis Transmembrane Conductance Regulator Biosynthesis and Function
Vol. 51, No. 3 (2014), pp. 354-362.
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Annals of ATS

Improvement in Quality of Life after Therapy for Mycobacterium abscessus Group Lung Infection. A Prospective Cohort Study
Vol. 13, No. 1 (2016), pp. 40-48.
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Proton Magnetic Resonance Imaging for Initial Assessment of Isolated Mycobacterium avium Complex Pneumonia
Vol. 13, No. 1 (2016), pp. 49-57.
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Considerations for the Conduct of Clinical Trials with Antiinflammatory Agents in Cystic Fibrosis. A Cystic Fibrosis Foundation Workshop Report
Vol. 12, No. 9 (2015), pp. 1398-1406.
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Pulmonary Exacerbations in Children with Cystic Fibrosis
Vol. 12, No. Supplement 2 (2015), pp. S200-S206.
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Rate of Uptake of Ivacaftor Use after U.S. Food and Drug Administration Approval among Patients Enrolled in the U.S. Cystic Fibrosis Foundation Patient Registry
Vol. 12, No. 8 (2015), pp. 1146-1152.
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Multiple-Breath Washout as a Lung Function Test in Cystic Fibrosis. A Cystic Fibrosis Foundation Workshop Report
Vol. 12, No. 6 (2015), pp. 932-939.
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Adherence Determinants in Cystic Fibrosis: Cluster Analysis of Parental Psychosocial, Religious, and/or Spiritual Factors
Vol. 12, No. 6 (2015), pp. 838-846.
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Fine Particulate Matter Exposure and Initial Pseudomonas aeruginosa Acquisition in Cystic Fibrosis
Vol. 12, No. 3 (2015), pp. 385-391.
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Inhaled Aztreonam Lysine versus Inhaled Tobramycin in Cystic Fibrosis. An Economic Evaluation
Vol. 12, No. 7 (2015), pp. 1030-1038.
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ClinicianATS Statements, Guidelines and Reports

ATS Statements, Guidelines and Reports are printed in the American Journal of Respiratory and Critical Care Medicine. These documents are also available in PDF format. You may download one copy of any ATS document; there is no charge for this service. For examples, please Click Here.