Cystic Fibrosis

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Information for Experts

Cystic Fibrosis Week


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ClinicianATS Journal articles on Cystic Fibrosis



Regulation of IL-4 Receptor Signaling by STUB1 in Lung Inflammation
Vol. 189, No. 1 (2014), pp. 16-29
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Malfolded Protein Structure and Proteostasis in Lung Diseases
Vol. 189, No. 1 (2014), pp. 96-103
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Efficacy and Safety of Ivacaftor in Patients Aged 6 to 11 Years with Cystic Fibrosis with a G551D Mutation
Vol. 187, No. 11 (2013), pp. 1219-1225
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Inhalation Treatment with Glutathione in Patients with Cystic Fibrosis. A Randomized Clinical Trial
Vol. 188, No. 1 (2013), pp. 83-89.
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A Clinical Prediction Tool for Prognosis in Patients with Cystic Fibrosis, Short-Term Glucocorticoid Therapy for Chronic Obstructive Pulmonary Disease, and Laryngeal Ultrasound for Prediction of Postextubation Laryngeal Edema
Vol. 189, No. 4 (2014), pp. 482-483.
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Lack of Neutrophil Elastase Reduces Inflammation, Mucus Hypersecretion, and Emphysema, but Not Mucus Obstruction, in Mice with Cystic Fibrosis–like Lung Disease
Vol. 189, No. 9 (2014), pp. 1082-1092.
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Measuring Mucociliary Transport and Mucus Properties in Multiple Regions of Airway Epithelial Surfaces Helps Clarify Cystic Fibrosis Defects
Vol. 190, No. 4 (2014), pp. 364-365.
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In Vivo X-Ray Imaging Reveals Improved Airway Surface Hydration after a Therapy Designed for Cystic Fibrosis
Vol. 190, No. 4(2014), pp. 469-472.
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Magnetic Resonance Imaging Detects Changes in Structure and Perfusion, and Response to Therapy in Early Cystic Fibrosis Lung Disease
Vol. 189, No. 8 (2014), pp. 956-965.
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High Expression of Midkine in the Airways of Patients with Cystic Fibrosis
Vol. 49, No. 6 (2013), pp. 935-942
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Cystic Fibrosis Therapy: A Community Ecology Perspective
Vol. 48, No. 2 (2013), pp. 150-156
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Low Sphingosine-1–Phosphate Impairs Lung Dendritic Cells in Cystic Fibrosis
Vol. 48, No. 2 (2013), pp. 250-257
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H2O2 Stimulates Cystic Fibrosis Transmembrane Conductance Regulator through an Autocrine Prostaglandin Pathway, Using Multidrug-Resistant Protein–4
Vol. 49, No. 4 (2013), pp. 672-679
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Immune Responses in Cystic Fibrosis
Are They Intrinsically Defective?
Vol. 46, No. 6 (2012), pp. 715-722
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Activation of P2RY11 and ATP Release by Lipoxin A4 Restores the Airway Surface Liquid Layer and Epithelial Repair in Cystic Fibrosis
Vol. 51, No. 2 (2014), pp. 178-190.
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Synthetic Aminoglycosides Efficiently Suppress Cystic Fibrosis Transmembrane Conductance Regulator Nonsense Mutations and Are Enhanced by Ivacaftor
Vol. 50, No. 4 (2014), pp. 805-816.
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A Genomic Signature Approach to Rescue ΔF508-Cystic Fibrosis Transmembrane Conductance Regulator Biosynthesis and Function
Vol. 51, No. 3 (2014), pp. 354-362.
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What to Expect When You’re Expectorating: Cystic Fibrosis Exacerbations and Microbiota
Vol. 10, No.3 (2013), pp. 249-250
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Long-term Effects of Pregnancy and Motherhood on Disease Outcomes of Women with Cystic Fibrosis
Vol. 10, No. 3 (2013), pp. 213-219
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Changes in Cystic Fibrosis Airway Microbiota at Pulmonary Exacerbation
Vol. 10, No. 3 (2013), pp. 179-187
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Antibiotic Management of Lung Infections in Cystic Fibrosis. II. Nontuberculous Mycobacteria, Anaerobic Bacteria, and Fungi
Vol.11, (2014) pp. 1298-1306
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Quality Improvement Initiative to Reduce Deep Vein Thrombosis Associated with Peripherally Inserted Central Catheters in Adults with Cystic Fibrosis
Vol. 11, No. 9 (2014), pp. 1404-1410
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Cystic Fibrosis Foundation Pulmonary Guideline. Pharmacologic Approaches to Prevention and Eradication of Initial Pseudomonas aeruginosa Infection
Vol. 11, No. 10 (2014), pp. 1640-1650
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